Menetrier disease: Case report with video

Authors

  • Martín Alonso Gómez Zuleta Universidad Nacional de Colombia, Hospital Universitario Nacional de Colombia
  • Oscar Fernando Ruíz Morales Hospital Universitario Nacional de Colombia
  • Javier Riveros Hospital Universitario Nacional de Colombia

DOI:

https://doi.org/10.22516/25007440.396

Keywords:

Menetrier disease, mucosal hypertrophy, hypoalbuminemia

Abstract

Menetrier disease (also known as giant hypertrophic gastritis or hypoproteinemic hypertrophic gastropathy) is a rare entity characterized by protein losing enteropathy, hypochlorhydria and thickening of the mucosal folds of the fundus and the gastric corpus. Its constellation of classic symptoms includes nausea, vomiting, abdominal pain and peripheral edema, and it is associated with increased risk of gastric cancer. Nevertheless, its pathophysiology is not yet fully understood and clinical and endoscopic diagnosis can be difficult to establish. This article describes a clinical case and provides a brief review of the literature.

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Author Biographies

Martín Alonso Gómez Zuleta, Universidad Nacional de Colombia, Hospital Universitario Nacional de Colombia

Medico internista y gastroenterólogo, Hospital Universitario Nacional de Colombia, Universidad Nacional de Colombia, Unidad de gastroenterología y ecoendoscopia (UGEC). Bogotá, Colombia

Oscar Fernando Ruíz Morales, Hospital Universitario Nacional de Colombia

Medico internista y gastroenterólogo, Hospital Universitario Nacional de Colombia, Unidad de gastroenterología y ecoendoscopia (UGEC). Bogotá, Colombia.

Javier Riveros, Hospital Universitario Nacional de Colombia

Medico internista y gastroenterólogo, Hospital Universitario Nacional de Colombia, Unidad de gastroenterología y ecoendoscopia (UGEC). Bogotá, Colombia.

References

Ménétrier P. Des polyadenomes gastriques et leur rapport avecle cancer de l›estomac. Arch Physiol Norm Pathol. 1888;1:236-62.

Rich A, Toro TZ, Tanksley J, Fiske WH, Lind CD, Ayers GD, et al. Distinguishing Ménétrier’s disease from its mimics. Gut. 2010;59(12):1617-24. https://doi.org/10.1136/gut.2010.220061

Coffey RJ Jr, Tanksley J. Pierre Ménétrier and his disease. Trans Am Clin Climatol Assoc. 2012;123:126-33.

Huh WJ, Coffey RJ, Washington MK. Ménétrier’s Disease: Its Mimickers and Pathogenesis. J Pathol Transl Med. 2016;50(1):10-6. https://doi.org/10.4132/jptm.2015.09.15

Patel M, Mottershead M. Disease recurrence following cetuximab completion and declining a gastrectomy: what next to manage Ménétriers disease? BMJ Case Rep. 2014;2014. pii: bcr2014204954. https://doi.org/10.1136/bcr-2014-204954

Fiske WH, Tanksley J, Nam KT, Goldenring JR, Slebos RJ, Liebler DC, et al. Efficacy of cetuximab in the treatment of Menetrier’s disease. Sci Transl Med. 2009;1(8):8ra18. https://doi.org/10.1126/scitranslmed.3000320

Azer M, Sultan A, Zalata K, Abd El-Haleem I, Hassan A, El-Ebeidy G. A case of Menetrier’s disease without Helicobacter pylori or hypoalbuminemia. Int J Surg Case Rep. 2015;17:58-60. https://doi.org/10.1016/j.ijscr.2015.10.025

Silva PH, Rigo P, Batista RP, Toma RK, Oliveira LA, Suzuki L. Ménétrier’s disease associated with gastric adenocarcinoma in a child - imaging aspect. Rev Assoc Med Bras (1992). 2016;62(6):485-9. https://doi.org/10.1590/1806-9282.62.06.485

Published

2019-07-02

How to Cite

Gómez Zuleta, M. A., Ruíz Morales, O. F., & Riveros, J. (2019). Menetrier disease: Case report with video. Revista Colombiana De Gastroenterología, 34(2), 190–193. https://doi.org/10.22516/25007440.396

Issue

Section

Case report

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